Trimethylaminuria (TMAU), also known as fish odor syndrome or fish malodor syndrome, is a rare metabolic disorder that causes a defect in the normal production of an enzyme named flavin-containing monooxygenase 3 (FMO3). When FMO3 is not working correctly or if not enough enzyme is produced, the body loses the ability to properly convert trimethylamine (TMA) from precursor compounds in food digestion into trimethylamine oxide (TMAO), through a process called N … WebTrimethylaminuria is also known as ‘fish (mal)odour syndrome ’ because of the characteristic fishy body odour. Trimethylamine is a volatile aliphatic molecule, best …
Things That Can Affect the Smell of Your Pee
WebJan 9, 2024 · An uncommon condition that's also known as "fish odour syndrome". Sufferers are unable to turn a strong-smelling chemical produced in the gut, when bacteria break down certain foods, into a ... WebNov 5, 2024 · Clinical characteristics. Primary trimethylaminuria is characterized by a fishy odor resembling that of rotten or decaying fish that results from excess excretion of trimethylamine in the urine, breath, … hoffer school
Trimethylaminuria - wikidoc
Webrimethylaminuria, or fish odor syndrome (FOS), is a condition characterized by the presence of trimethylamine (TMA)—a tertiary amine whose odor is described as resembling that of rotting fish—in the urine, sweat, and expired air. The cause of the syndrome is rooted in the dysfunctional metabolism of TMA,1 which is normally oxidized by ... WebApr 13, 2024 · Tyrosinemia is treated with medicine and a low-tyrosine diet. Fish Odor Syndrome . 15/16 . Also called trimethylaminuria, this genetic condition can give your pee a fishy smell. It happens when ... WebTrimethylaminuria causes the body to produce a fishy odor that is released in the sweat, urine, breath, and reproductive fluids. People with Trimethylaminuria are unable to … https fb facebook